question

The name of the condition that develops in up to 5% of newborns with darkly pigmented skin with prominent pustules without erythema that rupture, leaving a collarette of scale and hyperpigmentation, located on forehead, chin, neck, back, shins, or widespread that may last several month? Smear of the pustule shows? Histology shows?

answer

Transient Neonatal Pustular Melanosis; PMN; subcorneal pustule with PMNS

question

The name of the condition that develops within 24-48 hours after birth in 50% of full term infants on the face, trunk, limbs, buttocks (spares palms and soles) with blotchy erythematous macules, papules, pustules and wheals? Smear of pustule? History?

answer

Erythema Toxicum Neonatorum; eos; subcorneal pustule with eos (ass with pilosebaceous unit)

question

The name of the condition that occurs within the first 2-3 weeks of life as inflammatory non comedonal pustular eruption on cheeks mostly? Associated species in pathogenesis? Histology

answer

Neonatal Cephalic Pustulosis (neonatal acne) malassezia follicular pustules with PMNs

question

Form of panniculitis that occurs in severly ill premature infants within first week of life with diffuse cold, rigid, board like, woody hardening of skin sparing genitalia, palms, soles. What is the classic histology?

answer

Sclerema Neonatorum; needle shaped clefts in lipocyte with little inflammation

question

What three neonatal conditions are characterized histologically by formation of needle shaped clefts within lipocytes? Which type of crystal in each?

answer

Sclerema Neonatorum type A microsized crystal (normal but in excess with no associated inflammation); Subcutaneous fat necrosis of the newborn post steroid panniculitis type B crystals (rosette arrangement with associated inflammation)

question

Form of panniculitis that occurs in full term neonates within the first few weeks of life with circumscribed, erythematous, indurated subcutaneous nodules favoring cheeks, shoulders, back, buttocks, thighs. Histologically with needle shaped clefts in fat necrosis and prominent inflammatory infiltrate. What is the main associated symptom that should be monitored until 1 month after full resolution?

answer

subcutaneous fat necrosis of the newborn hypercalcemia

question

Soft, mostly non painful papules involving the heels. Common and infantile variant. What is the name of the condition and two diseases they are seen in?

answer

Pedal papules of infancy Ehlers Danlos Prader Willi

question

What is the name of the condition with ill defined erythematous patches with waxy scale over scalp, axillae, groin seen in infants typically 1 week after birth with resolution within 1 year? What are three etiologic links?

answer

Seborrheic Dermatitis active sebaceous glands abnormal sebum composition Malassezia Furfur

question

Name of condition that occurs in neonates less than 2 weeks of age, children and adults in hot climates who present with non pruritic clear fragile 1 mm vesicles on the face and trunk? Location of obstruction?

answer

Miliaria crystallina stratum corneum (obstruction of eccrine ducts)

question

Name of condition that occurs in neonates 1-3 weeks of age, children and adults in hot climates with non follicular pruritic erythematous 1-3 mm papules, pustules on the neck and upper trunk? Location of obstruction

answer

Miliaria rubra mid epidermis (eccrine ducts)

question

Name of condition that occurs in adults in hot climates with non pruritic white 1-3 mm papules on the trunk and proximal extremities? Hx of multiple bouts of ___? Location of obstruction?

answer

Miliaria Profunda Rubra DEJ (eccrine ducts)

question

The hair collar sign can be seen in infants born with aplasia cutis congenita and consists of a ring of dark long hair encircling lesions. This may be a marker of what?

answer

neural tube defect

question

The name of syndrome with ACC of lower extremities + EBDD

answer

Bart

question

The name of syndrome with ACC on scalp with skull ossification defect + extensive CMTC (cutis marmorata telangiectatic congenita) + limb defects (reductions, syndactylyl) + cardiac

answer

Adams Oliver

question

The name of syndrome with Bilateral temporal ACC + abnormal eyelashes + leonine faces + upward slanting eyebrows

answer

Seitles

question

The name of condition present at birth with dark purple to red reticular pattern on trunk/extremities with segmental distribution that persists upon warming the affected infant. 50% of time associated with anomalies -- which are the two most common?

answer

CMTC hypoplasia vascular malformations

question

The name of condition seen at birth in 1 in 250 new borns with intact bullae, erosion, callus or superficial ulceration on a non inflamed base?

answer

Sucking blister

question

Which three congenital infections of the newborn have "blueberry muffin lesions" (i.e. red blue papules nodules)

answer

CMV Rubella Toxoplasmosis

question

Blueberry muffin lesions are seen in congenital infections of the newborn as red blue papules and nodules. What do they represent?

answer

Extramedullary erythropoiesis in dermis

question

Which congenital infection of the newborn is the leading cause of deafness and mental retardation in the US? Which leads to 50% change of deafness?

answer

CMV Rubella

question

Which TORCH syndrome has histology with enlarged endothelial cells with intranuclear inclusions?

answer

CMV

question

Which TORCH syndrome has hemorrhagic and necrotic papules that favor the trunk (?blueberry muffin) and in 10-30% have chorioretinitis that leads to visual loss and 20% with neurologic manifestations?

answer

Toxoplasmosis

question

What does TORCHs stand for?

answer

Toxoplasmosis other (varicella) rubella CMV HSV syphilis

question

In toxoplasmosis the risk of transmission is greatest if mom is infected in third trimester but a more severe disease if contracted early on. In Rubella, severe birth defects are seen if infected in the first ____ weeks? For varicella the risk is within the first ____ weeks?

answer

16 20

question

What is the mortality rate of HSV congenital infection if left untreated?

answer

50-75

question

In which TORCHs syndrome do you see rhagades (radial periorificial mouth nose eyes anus scars from previous fissures), papulosquamous macules papules (like secondary syphillius) plus bullous lesions (symphilitic phemphigus) and erosive lesions; snuffles; LAD?

answer

Early syphillis

question

What is the hutchinson's triad seen in late syphilis?

answer

Interstitial keratitis hutchinsons teeth (peg shaped notced permanent incisors) neural deafness

question

What is the name of multiple rounded rudimentary cusps on permanent first molars that are seen in late congenital syphilis?

answer

Mulberry molars

question

What is Higoumenakis sign? Seen in which type of congenital syphilis?

answer

thickening of clavicle late

question

Neurosyphilis is classically a manifestation of tertiary syphilis but can occur at any stage of the disease and can be seen in early congentital syphilis. Tabes dorsalis affects up to a third of patients with neurosyphilis with loss of posterior column (vibratory and position) Argyll roberston pupils and occurs in ____ congential syphilis

answer

late

question

Which diaper dermatitis includes scrotum? which spares the inguinal folds? includes inguinal creases?

answer

Candida irritant psoriasis

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